Basilar impression within a complex cranio-cervical junction anomalies (CCJAs) in a child presenting with impending bulbar cervical dissociation
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Date
2008-11-16
Authors
Dr. Jamal M. Ghosheh
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Abstract
<p>The recognition of the congenital anomalies involving the base of the skull CCJ region is important because of their association with brain stem-spinal cord compression, spinal instability and spinal deformity. Other organ system anomalies may be associated with CCJAs as these systems share common embryonic development. A basilar impression with neural compression in a form of bulbar and cervical myelopathy with associated occipito-cervical rotational instability levelled to occipito-axial hypoplastic occipitalised atlas caudally, to brain stem medullar neural compression bulbar ward, was diagnosed in a 14 year old boy who was admitted and managed at MIH-Jerusalem.</p>
<p>The recognition of the congenital anomalies involving the base of the skull CCJ region is important because of their association with brain stem-spinal cord compression, spinal instability and spinal deformity. Other organ system anomalies may be associated with CCJAs as these systems share common embryonic development. A basilar impression with neural compression in a form of bulbar and cervical myelopathy with associated occipito-cervical rotational instability levelled to occipito-axial hypoplastic occipitalised atlas caudally, to brain stem medullar neural compression bulbar ward, was diagnosed in a 14 year old boy who was admitted and managed at MIH-Jerusalem.</p>
<p>The recognition of the congenital anomalies involving the base of the skull CCJ region is important because of their association with brain stem-spinal cord compression, spinal instability and spinal deformity. Other organ system anomalies may be associated with CCJAs as these systems share common embryonic development. A basilar impression with neural compression in a form of bulbar and cervical myelopathy with associated occipito-cervical rotational instability levelled to occipito-axial hypoplastic occipitalised atlas caudally, to brain stem medullar neural compression bulbar ward, was diagnosed in a 14 year old boy who was admitted and managed at MIH-Jerusalem.</p>